Prevalence of selected pediatric conditions in children with Pierre Robin sequence.
نویسندگان
چکیده
Pierre Robin sequence (PRS) is a congenital abnormality characterized by micrognathia and glossoptosis, with or without cleft palate. Patients with PRS may demonstrate various pediatric conditions such as associated syndromes, respiratory distress, feeding difficulties, or middle ear pathology. The purpose of this study was to determine, by means of a retrospective computerized review of patient records, the presence of these pediatric conditions in a sample of 55 confirmed patients with PRS. Five patients (9.1%) exhibited associated syndromes; 20 (36.4%) had respiratory distress requiring no assistance; and 10 (18.2%) exhibited severe respiratory distress requiring tracheotomy. A total of 30 patients (54.5%) had early feeding difficulties requiring mechanical assistance to maintain adequate nutrition, and 50 (90.9%) had multiple episodes of otitis media. Chi-square analysis revealed a statistically significant relationship between the presence of respiratory difficulties and the need for feeding assistance (P = 0.012); and a highly significant relationship between the presence of otitis media and subsequent myringotomy tube placement (P < 0.001). Pediatric dentists who treat children with PRS should be aware of these relationships when obtaining medical history before establishing strategies to implement a treatment plan.
منابع مشابه
Role of SOX9 in the Etiology of Pierre-Robin Syndrome
Objective(s:Cleft lip/palate are common congenital anomalies, affecting approximately 2/1000 live births. Pierre Robin Sequence is a subgroup of the cleft palate population. Chromosomal abnormalities near the SOX9 gene disrupt the regulation of this gene and prevent the SOX9 protein from properly controlling the development of facial structures, which leads to isolated PRS. The present study wa...
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ورودعنوان ژورنال:
- Pediatric dentistry
دوره 17 2 شماره
صفحات -
تاریخ انتشار 1995